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Diagnosis: Congenital hairy nevus
Description: Congenital nevomelanocytic nevus of the forehead with a pebbled surface and thick terminal hairs.
Morphology: Plaque
Site: Face
Sex: F
Age: 12
Type: Clinical
Submitted By: Shahbaz Janjua
Differential DiagnosisHistory:
This adolescent girl presented with a large dark brown plaque involving most of the forehead,
and the frontal scalp since birth. The pebbly surfaced plaque was covered with thick terminal hairs.
Congenital hairy nevi , also known as congenital nevomelanocytic nevi, are usually noted at birth or
soon thereafter. Only 5% of the lesions are multiple but the location and size of a congenital hairy
nevus may be variable. There is a significant potential for large congenital hairy nevi to become
malignant.